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Slovenska pediatrija 2010; 17: 19-23

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Review article


V. Rajić
Klinični oddelek za otroško hematologijo in onkologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana, Ljubljana, Slovenija


Lymphangiomas are benign malformations of the lymphatic system and one of the most frequent congenital vascular malformations. They represent approximately 6% of all benign tumours in children. In about half of the patients the lymphangiomas are already obvious at birth. During the first 2 years of life lymphangiomas are detected in 80 – 90% of cases. About 60% of all lymphangiomas are found in the head and neck region, primarily affecting the tongue and the floor of the mouth. Patients should be treated by a multidisciplinary team of physicians and health professionals familiar with lymphatic malformations. There are various management options: supportive, surgical, endovascular (sclerotherapy) and medications.

Key words: lymphangioma, lymphatic malformations, lymphangiogenesis, lymphoedema.