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Slovenska pediatrija 2019; 26: 284-287


Case report

BRUGADA SYNDROME IN CHILDREN: CASE REPORT

Barbara Rebernik
Zdravstveni dom Velenje, Velenje, Slovenija

Uroš Mazič
Kirurška klinika, Klinični oddelek za otroško kirurgijo in intenzivno terapijo, Univerzitetni klinični center Ljubljana, Bohoričeva ulica 20, Ljubljana, Slovenija

Abstract

A child with Brugada syndrome that clinically presented with characteristic electrocardiographic changes and syn­cope during fever is presented. The syndrome is associated with an increased risk for ventricular tachyarrhythmia and sudden cardiac death in young adults. In children, it is rare however the most frequent clinical presentation is syncope and/or sudden cardiac death during fever. The only effective treatment which reduces the risk of sud­den cardiac death in Brugada syndrome is the implantation of a cardioverter defibrillator.

Key words: Brugada syndrome, ventricular arrythmias, sud­den cardiac death, syncope, heart disease


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