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Slovenska pediatrija 2025; 32: 186-190

https://doi.org/10.38031/slovpediatr-2025-4-03en

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Review article

BULLOUS FORM OF IGA VASCULITIS: A CASE REPORT AND LITERATURE REVIEW

Valentina Koranter
Zdravstveni dom Radovljica, Radovljica, Slovenija

Nataša Toplak
Klinični oddelek za otroško alergologijo, revmatologijo in klinično imunologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana, Ljubljana, Slovenija in Katedra za pediatrijo, Medicinska fakulteta, Univerza v Ljubljani, Ljubljana, Slovenija

Abstract

Bullous skin involvement with necrosis in IgA vasculitis in children is rare. In most cases, systemic treatment is not required for isolated skin involvement, except in severe clinical presentations. This article presents a 4-year-old child with a severe necrotic bullous form of IgA vasculitis. The patient was treated with intravenous immunoglobulins and methylprednisolone. The disease outcome was excellent, with no long-term consequences of skin necrosis.

Key words: IgA vasculitis, Henoch-Schönlein purpura, bullous skin diseases, intravenous immunoglobulins, methylprednisolone