Valentina Koranter
Zdravstveni dom Radovljica, Radovljica, Slovenija
Nataša Toplak
Klinični oddelek za otroško alergologijo, revmatologijo in klinično imunologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana, Ljubljana, Slovenija in Katedra za pediatrijo, Medicinska fakulteta, Univerza v Ljubljani, Ljubljana, Slovenija
Abstract
Bullous skin involvement with necrosis in IgA vasculitis in children is rare. In most cases, systemic treatment is not required for isolated skin involvement, except in severe clinical presentations. This article presents a 4-year-old child with a severe necrotic bullous form of IgA vasculitis. The patient was treated with intravenous immunoglobulins and methylprednisolone. The disease outcome was excellent, with no long-term consequences of skin necrosis.
Key words: IgA vasculitis, Henoch-Schönlein purpura, bullous skin diseases, intravenous immunoglobulins, methylprednisolone